Affiliations: Department of Orthopedics, The People's Hospital of Three Gorges University, The First People's Hospital of Yichang, Yichang, Hubei, China
Correspondence:
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Corresponding author: Weifei Wu, Department of Orthopedics, The People's Hospital of Three Gorges University, The First People's Hospital of Yichang, Yichang, Hubei, China. Tel.: +86 15171791236; E-mail:[email protected]
Abstract: BACKGROUND: The syrinx can occur in any region of the spinal cord
and is common in cervical and/or thoracic region, and distributing along
spinal cord is unusual, especially association with Chiari II malformation
and scoliosis. OBJECTIVE: To report a first case of entire syringomyelia
associated with Chiari II malformation and severe scoliosis and
hydrocephalus. CASE PRESENTATION: The patient began to experience symptoms of
bilateral hand weakness in adulthood. In this patient, MR imaging of the
brain and spine showed syrinx along entire spine and hydrocephalus,
cerebellar tonsillar herniation, and expansion of the fourth ventricle and
posterior cranial fossa. The patient underwent operative treatment to
prevent the progression of her neurological deficit. At 12 months'
follow-up, the patient's neurological deficit remains stable with the
scoliosis left untreated. CONCLUSIONS: Foramen magnum decompression, duraplasty and
syrinx-shunting are effective methods even to CM II and entire syrinx.
Keywords: Entire syringomyelia, Chiari II malformation, severe scoliosis, hydrocephalus
