First report on hemispherotomy in two Tunisian patients with Rasmussen syndrome

Article type: Research Article

Authors: Méziou, Meriam^; | Kamoun, Fatma^; | Ellouz, Emna^; | Hsairi, Ines^; | Mnif, Zeineb^; | Delalande, Olivier | Boudawara, Mohamed Zaher^; | Triki, Chahnez^;

Affiliations: Department of Child Neurology, Hedi Chaker Hospital, Sfax, Tunisia | Research Unit of Neuropediatrics, Sfax, Tunisia | Department of Radiology, Hedi Chaker Hospital, Sfax, Tunisia | Rothschild Foundation, Paris, France | Department of Neurosurgery, Habib Bourguiba Hospital, Sfax, Tunisia

Note: [] Correspondence: Dr. Chahnez Triki, Department of Child Neurology, Hedi Chaker Hospital-Sfax, Tunisia. Tel.: +216 74 242 564; Fax: +216 74 242 564; E-mail: [email protected]

Abstract: Rasmussen syndrome is a rare cryptogenic progressive brain disorder causing severe neurological problems. Surgery, particularly hemispherectomy in any of its varied forms, has an excellent effect in controlling seizures. We report two Tunisian patients with classically sporadic and unilateral childhood form. They are both treated successfully with vertical parasagittal hemispherotomy. This paper discusses and reviews the advances in epilepsy surgery for Rasmussen syndrome.

Keywords: Rasmussen syndrome, hemispherectomy, hemispherotomy, vertical approch

DOI: 10.3233/JPN-2011-0474

Journal: Journal of Pediatric Neurology, vol. 9, no. 2, pp. 277-280, 2011