Radiological features of genitourinary plexiform neurofibroma in three patients

Article type: Research Article

Authors: Mansour, Asem H. | Haikal, Ali H. | Omari, Hamzi Z. | Nofal, Abdallah J. | Swaidan, Maisa Y.^;

Affiliations: Department of Diagnostic Radiology, King Hussein Cancer Center, Amman, Jordan | Department of Diagnostic Radiology, King Hussein Medical Center, Amman, Jordan

Note: [] Corresponding author: Maisa Y. Swaidan, Consultant radiologist at King Hussein Cancer Centre, Queen Rania Al Abdullah Street, P.O. Box 1269 Al-Jubeiha Amman, 11941 Jordan. Tel.: +962 6 5300460 ext: 1222; Fax: +962 6 5342567; E-mail: [email protected].

Abstract: We report three female pediatric patients with plexiform neurofibromas affecting the genitourinary system. We describe the characteristic imaging findings of genitourinary plexiform neurofibromas. For the first time we describe a distinctive radiologic sign of vaginal involvement which we called “Mercedes-Benz sign” due to the resemblance in appearance at the axial plane.

Keywords: Plexiform neurofibroma, genitourinary, Mercedes-Benz sign, pediatrics

DOI: 10.3233/PNR-2012-036

Journal: Journal of Pediatric Neuroradiology, vol. 1, no. 4, pp. 287-292, 2012